Klippel-Trenaunay syndrome is a congenital peripheral vascular disease. In 1900, the French doctor Klippel, Trenaunay first reported, named
Klippel-Trenaunay syndrome is a congenital peripheral vascular disease. In 1900, the French doctor Klippel, Trenaunay first reported, named "hypertrophic varicose nevus". In addition, there are many other names: Klippel-Trenaunay-Weber syndrome, Weber syndrome, Ollierklippel syndrome, Trenaunay syndrome, Parkes-Weber syndrome, vascular bone hypertrophy syndrome, hypertrophic hemangioma syndrome, hypertrophic verrucous nevus, hypertrophic vascular dilatation, mainly as a congenital vascular abnormal performance.
There is no special treatment, mainly symptomatic reduction.
Such as limb length difference of more than 1.9cm, but the contralateral heel pad, to prevent long-term complications.
Thickening of the affected limb, should use medical elastic stockings or elastic bandage compression treatment, this method can control the varices, relieve the venous congestion caused by lower limb heaviness and swelling, prevent the occurrence of superficial thrombophlebitis.
For deep vein patency, varicose veins and normal venous valve function, can board varicose sclerotherapy or laser treatment of superficial. However, the deep vein of patients, this method does not apply.
The arteriovenous fistula or bilateral limb discrepancy of children, can advance bilateral lower extremity angiography, abnormal blood vessels can be found, but the effect is short, embolism, non dominant fistula will "wake up" and even open; open surgery is "dead therapy", in order to delay limb development, reduce the purpose of lameness however, big investment, low efficiency, also in danger of limb muscle necrosis. Treatment need to be cautious.
Treatment of cavernous hemangioma in children with hemangioma.