Jeavons syndrome (eyelid myoclonia with absences)

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(eyelid myoclonia with eyelid myoclonia with absences absences, EMA) was first proposed by Jeavons in 1977. He described it as the eyelid my

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(eyelid myoclonia with eyelid myoclonia with absences absences, EMA) was first proposed by Jeavons in 1977. He described it as the eyelid myoclonus with short absence of epilepsy syndrome, the EEG features due to the closed eyes and the light sensitivity to the generalization of the symmetry of electrical activity. It has been suggested that E M A should be named "Jeavons syndrome" as an independent epilepsy syndrome in idiopathic generalized epilepsy (idiopathic generalized epilepsies, IGEs). Eyelid myoclonia with or without absence seizures, in 2001 the international classification of epileptic seizures was included as a separate type of comprehensive epilepsy.

Jeavons syndrome and clinical manifestation is paroxysmal brief, rapidly repeated eyelid clonic contraction, no obvious loss of consciousness or only mild disturbance of consciousness (with absence), EEG synchronization occurs generalized high amplitude 3 ~ 5 Hz spikes or spike wave discharges, the short duration (1 to 5 seconds), often by the closing action induced characteristic, in fact all patients are sensitive.

Jeavons syndrome is thought to belong to the IGE in a separate syndrome, according to previous reports, it is regarded as a kind of idiopathic myoclonus syndrome. The main clinical features are myoclonia in the same patient, can appear alone or in temporary absence seizures, mainly by eyes and light stimulation. As a kind of light sensitive epilepsy, patients often self induced.

The syndrome need long-term antiepileptic drug therapy is the first choice, second choice of ethosuximide, valproic acid, lamotrigine. Sustained frequent seizures needed treatment, valproic acid and ethosuximide or clonazepam or lamotrigine combined therapy. Clonazepam better on eyelid myoclonic seizure effect.

 

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